Serveur d'exploration sur le lymphœdème

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Pediatric lymphedema and correlated syndromes: Role of microsurgery

Identifieur interne : 006D72 ( Main/Exploration ); précédent : 006D71; suivant : 006D73

Pediatric lymphedema and correlated syndromes: Role of microsurgery

Auteurs : Corradino Campisi [Italie] ; Elisa Da Rin [Italie] ; Carlo Bellini [Italie] ; Eugenio Bonioli [Italie] ; Francesco Boccardo [Italie]

Source :

RBID : ISTEX:96F5700F67240DD7039C0C14BEB1AEFDDA03D8A4

Descripteurs français

English descriptors

Abstract

Authors report modern diagnostic and therapeutic procedures used in the correct assessment and treatment of congenital lymphatic and chylous disorders. Lymphatic dysplasias can be clinically represented only by peripheral lymphedema or be associated with more complex dysfunctions of chyliferous vessels and the thoracic duct (chylous ascitis, chylothorax, etc.) It is, therefore, useful to perform a complete diagnostic evaluation of each patient before carrying out any therapeutical approach. Lymphoscintigraphy, lymphangio‐MR, oil contrast lymphography, and lymphangio‐CT are the common diagnostic tools used in these cases, variable associated depending above all on the complexity of the pathology. From the therapeutical point of view, microsurgical methods proved to bring successful and long lasting results, both with derivative lymphatic‐venous anastomoses and reconstructive lymphatic‐venous‐lymphatic anastomoses. Better long‐term results are obtained in earlier stages. © 2008 Wiley‐Liss, Inc. Microsurgery, 2008.

Url:
DOI: 10.1002/micr.20466


Affiliations:


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<div type="abstract" xml:lang="en">Authors report modern diagnostic and therapeutic procedures used in the correct assessment and treatment of congenital lymphatic and chylous disorders. Lymphatic dysplasias can be clinically represented only by peripheral lymphedema or be associated with more complex dysfunctions of chyliferous vessels and the thoracic duct (chylous ascitis, chylothorax, etc.) It is, therefore, useful to perform a complete diagnostic evaluation of each patient before carrying out any therapeutical approach. Lymphoscintigraphy, lymphangio‐MR, oil contrast lymphography, and lymphangio‐CT are the common diagnostic tools used in these cases, variable associated depending above all on the complexity of the pathology. From the therapeutical point of view, microsurgical methods proved to bring successful and long lasting results, both with derivative lymphatic‐venous anastomoses and reconstructive lymphatic‐venous‐lymphatic anastomoses. Better long‐term results are obtained in earlier stages. © 2008 Wiley‐Liss, Inc. Microsurgery, 2008.</div>
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